THE "CAPS" REGISTRY-4
Table 4. Thrombotic
clinical manifestations of patients at the time of catastrophic APS.
|
PATIENT No.
|
HEPATIC |
GASTROINTESTINAL |
SPLENIC |
||||||
|
|
CLINICAL
|
IMAGING |
BIOPSY
|
CLINICAL |
IMAGING |
BIOPSY
|
CLINICAL |
IMAGING |
BIOPSY
|
|
1 |
|
|
|
|
|
|
|
|
|
|
2 |
|
|
|
|
|
|
|
|
|
|
3 |
|
|
|
|
|
|
|
|
|
|
4 |
|
|
Microthrombi |
|
|
|
|
|
|
|
5 (1st) |
|
|
|
|
|
|
|
|
|
|
5 (2nd) |
|
|
|
|
|
|
|
|
|
|
6 |
|
|
Focal
dilatation sinusoids |
|
|
Microthrombi |
|
|
|
|
7 |
EEL |
|
|
Pain |
Superior mesenteric stenosis |
|
|
|
|
|
8 |
|
|
Thrombi |
|
|
|
|
|
|
|
9 |
Pain |
|
Sinusoids thrombi Portal thrombi |
|
|
|
|
|
|
|
10 |
Pain |
|
Sinusoids thrombi Portal thrombi |
|
|
|
|
|
|
|
11 |
Yes |
|
|
Yes |
|
|
|
|
|
|
12 |
|
|
|
Hemorrhage |
|
|
Splenomegaly |
Splenomegaly |
Microthombi |
|
13 |
|
|
|
|
|
|
|
|
|
|
14 |
|
Portal thrombi |
|
|
|
|
|
|
|
|
15 |
EEL |
|
|
|
|
|
|
|
|
|
16 |
|
|
Portal thrombi |
|
|
|
|
|
|
|
17 |
Yes |
|
|
|
|
|
Yes |
|
|
|
18 |
|
|
|
|
|
Microthrombi |
|
|
|
|
19 |
|
|
|
|
|
|
|
|
Infart |
|
20 |
|
|
|
Pain |
|
|
|
|
|
|
21 (1st) |
|
|
|
Pain |
Pechechies |
|
|
|
|
|
(2nd) |
|
|
|
|
|
|
|
|
|
|
22 |
EEL
|
|
|
|
|
|
|
|
Large infart |
|
23 |
|
|
|
|
|
|
|
|
|
|
24 |
Hepatomegaly |
|
|
|
|
|
|
|
|
|
25 |
Yes
|
|
|
Yes |
|
|
Yes |
|
|
|
26 |
|
|
|
|
|
|
|
|
|
|
27 |
|
|
|
|
|
|
|
|
|
|
28 |
|
|
|
Pain |
Mesenteric thrombi |
|
|
|
|
|
29 |
|
|
|
Yes |
|
|
|
|
|
|
30 |
EEL Hepatomegaly |
|
|
Pain |
Mesenteric artery
occlusion |
Mesenteric artery
thrombi |
|
Splenic artery occlusion |
thrombi |
|
31 |
EEL |
|
|
Pain |
|
|
|
|
|
|
32 |
|
|
|
|
|
|
|
|
|
|
33 |
Pain EEL |
|
|
Pain |
Bowel ischemia |
|
|
|
|
|
34 |
|
|
|
|
|
|
|
|
|
|
35 |
Hepatomegaly |
|
|
|
|
|
|
|
|
|
36 |
|
|
|
|
|
Microthrombi |
|
|
Microthrombi |
|
37 |
|
|
|
Yes |
|
|
|
|
|
|
38 |
Yes |
|
|
|
|
|
|
|
|
|
39 |
|
|
|
Yes |
|
|
|
|
|
|
40 |
|
|
|
|
|
|
|
|
|
|
41 |
|
|
|
|
|
|
|
|
|
|
42 |
|
|
|
|
|
|
|
|
|
|
43 |
|
|
|
|
|
|
|
|
|
|
44 |
|
|
|
|
|
|
|
|
|
|
45 |
|
|
|
|
|
|
|
|
|
|
46 |
|
|
|
|
|
|
|
|
|
|
47 |
|
|
Microinfarcts
|
|
|
|
|
|
|
|
48 |
|
|
|
|
|
|
|
|
|
|
49 |
|
|
|
|
|
|
|
|
|
|
50 |
Pain |
Ischemia |
|
Pain |
Ischemia |
Microthrombi |
Pain |
ischemia |
|
|
51 |
Pain EEL |
Portal
thrombi |
Ischemia |
|
Vein
thrombi |
|
|
Vein
thrombi |
|
|
52 |
Pain jaudince |
Portal thrombi |
Nodular regenerative
hyperplasia |
|
|
|
|
|
|
|
53 |
|
|
|
|
|
|
|
|
Microthrombi |
|
54 |
|
|
|
|
|
Microthrombi |
|
|
|
|
55 |
|
|
|
|
|
|
|
|
|
|
56 |
|
|
|
|
|
|
|
|
|
|
57 |
EEL |
|
|
|
|
|
|
|
|
|
58 |
|
Periportal microinfarcts |
|
|
|
|
|
|
|
|
59 |
Pain Ascites |
Hepatomegaly IVC stenosis |
Budd-chiari |
|
|
|
|
|
|
|
60 |
|
Infarcts |
|
|
|
|
|
|
|
|
61 |
|
|
|
|
|
|
|
|
|
|
62 |
EEL |
|
|
Pain |
|
Microthrombi |
|
|
|
|
63 |
|
|
|
|
|
|
|
|
|
|
64 |
|
|
|
|
|
|
|
|
|
|
65 |
Failure Hepatomegaly |
Portal & hepatic
vein thrombi |
|
|
Superior mesenteric
artery thrombi |
|
|
|
|
|
66 |
Pain |
Microinfarcts |
microthrombisis |
|
|
|
|
|
|
|
67 |
|
|
|
|
Mesenteric artery
thrombi |
|
|
|
|
|
68 |
|
|
|
Hemorrhage |
|
Microthrombi |
|
|
Microthrombi |
|
69 |
|
|
|
|
|
Microthrombi |
|
|
Microthrombi |
|
70(1st) |
EEL |
|
|
|
|
|
|
Splenomegaly |
|
|
(2nd) |
|
|
|
|
|
|
|
|
|
|
(3rd) |
EEL |
|
|
|
|
|
|
|
|
|
71 |
Pain |
Infarcts |
|
Pain |
Infarcts |
|
|
|
|
|
72 |
Failure |
Perfusion defects |
|
|
|
|
|
Pefusion defects
|
|
|
73 |
EEL |
|
|
|
|
|
|
|
|
|
74 |
|
|
|
|
|
|
|
|
|
|
75 |
|
|
|
|
|
|
|
|
|
|
76 |
|
|
|
|
|
|
|
|
|
|
77 |
Yes |
|
|
|
|
|
|
|
|
|
78 |
|
|
|
|
|
|
|
|
|
|
79 |
|
|
|
|
|
|
|
|
|
|
80 |
|
|
|
|
|
|
|
|
|
|
81 |
|
|
|
|
|
|
|
|
|
|
82 |
|
|
|
|
|
|
|
|
|
|
83(1st) |
EEL |
|
|
|
|
|
|
|
|
|
83(2nd) |
EEL |
|
|
|
|
|
|
|
|
|
84 |
|
|
|
|
|
|
|
|
|
|
85 |
|
|
|
|
|
Microthrombi |
|
|
Microthrombi |
|
86 |
|
|
|
|
Thrombi |
|
|
|
|
|
87 |
|
|
|
|
|
|
|
|
|
|
88 |
|
|
|
|
|
|
|
|
|
|
89 |
|
|
|
|
|
|
|
|
|
|
90 |
|
|
|
|
|
|
|
|
|
|
91 |
|
|
|
|
|
|
|
|
Microthrombi |
|
92 |
|
|
Microthrombi |
|
|
|
|
|
|
|
93 |
|
|
|
|
|
|
|
|
|
|
94 |
|
|
|
|
|
|
|
|
|
|
95 |
|
|
|
|
|
|
|
|
Microthrombi |
|
96 |
|
|
|
|
|
|
|
Multiple infarcts |
Microthrombi |
|
97 |
|
|
|
|
|
|
|
|
|
|
98 |
|
Infarct |
|
|
Infarct |
|
|
|
|
|
99 |
|
|
|
|
|
|
|
|
|
|
100 |
|
|
|
|
|
|
|
|
|
|
101 |
|
|
|
|
Superior mesenteric
artery thrombi |
|
|
Infarct |
|
|
102 |
EEL |
|
|
Hemorrhage |
|
|
|
|
|
|
103 |
EEL |
Hepatomegaly |
|
|
|
|
|
|
|
|
104 |
|
|
|
|
|
|
|
|
|
|
105 |
EEL Jaundice |
|
|
|
|
|
|
|
|
|
106 |
|
|
|
|
|
|
|
|
|
|
107 |
|
|
|
|
|
Gastric ischemia |
|
|
|
|
108 |
|
|
|
|
|
|
|
|
|
|
109 |
|
|
|
|
Mesenteric thickened |
|
|
|
|
|
110 |
|
|
|
|
|
|
|
|
|
|
111 |
Jaundice Pain |
Hepatomegaly vein thrombi |
|
|
|
|
|
|
|
|
112 |
EEL |
|
|
|
|
|
|
Vein thrombi Infarcts |
|
|
113 |
Jaundice EEL |
Infarcts |
|
|
|
|
|
Infarcts |
|
|
114 |
|
|
|
|
Ischemic necrosis |
|
|
|
|
|
115 |
EEL |
|
|
Pain
|
|
Microthrombi |
Pain |
Infarcts |
|
|
116 |
Jaundice EEL |
|
Infarcts |
|
|
|
|
|
|
|
117 |
|
|
|
|
|
|
|
|
|
|
118 |
|
Budd-chiari |
|
|
|
|
|
|
|
|
119 |
EEL |
|
|
|
|
|
|
|
|
|
120 |
|
|
|
|
|
|
|
|
|
|
121 |
EEL |
|
|
|
|
|
|
|
|
|
122 |
|
|
|
|
Thrombi |
|
|
|
|
|
123 |
|
|
|
|
Gut perforation |
|
|
Infarcts |
Infarcts |
|
124 |
|
|
|
|
Purpuric lesions |
|
|
|
|
|
125 |
|
|
|
|
|
|
|
|
|
|
126 |
|
|
|
|
|
|
|
|
|
|
127 |
|
|
|
Yes |
|
|
|
|
|
|
128 |
|
|
|
|
|
|
|
|
|
|
129 |
|
|
|
|
|
|
|
|
|
|
130 |
|
|
|
|
|
|
|
|
|
|
131 |
|
|
|
|
|
|
|
|
Múltiple infarcts |
|
132 |
|
|
|
|
|
|
|
|
|
|
133 |
EEL |
|
|
|
|
|
|
|
|
|
134 |
|
Thrombi |
|
|
|
|
|
Thrombi |
|
|
135 |
|
|
|
Paralytic ileus |
|
|
|
|
|
|
136 |
|
|
|
|
|
||||