THE
"CAPS" REGISTRY-2
Table 2. Thrombotic clinical manifestations of patients at the time of
catastrophic APS.
|
PATIENT No. |
PERIPHERAL |
CARDIAC |
PULMONARY |
|||||
|
|
VENOUS |
ARTERIAL |
CLINICAL |
IMAGING |
BIOPSY |
CLINICAL |
IMAGING |
BIOPSY |
|
1 |
|
|
Failure |
|
|
|
|
|
|
2 |
DVT |
|
|
|
|
ARDS |
Bilateral infiltrates |
|
|
3 |
|
|
Failure
|
|
|
ARDS |
|
|
|
4 |
|
|
|
|
L-S Microthrombosis |
|
|
Microthrombosis |
|
5 (1st) |
|
|
|
LV |
|
|
|
|
|
5 (2nd) |
|
|
|
|
LV Microthrombosis |
|
|
Edema
|
|
6 |
|
|
|
|
Microthrombosis |
|
|
|
|
7 |
|
|
|
|
|
|
|
|
|
8 |
|
|
Failure
|
L-S |
Microthrombosis |
|
Edema
|
|
|
9 |
|
|
|
|
|
|
|
|
|
10 |
|
|
|
|
|
|
|
|
|
11 |
DVT |
|
|
|
|
|
PE |
|
|
12 |
|
|
|
|
|
|
|
|
|
13 |
|
|
|
|
|
|
|
Microthrombosis |
|
14 |
|
|
|
|
|
ARDS |
Diffuse
infiltrate |
|
|
15 |
|
|
|
|
|
Dyspnea |
Edema |
|
|
16 |
|
|
|
|
LS
Microinfarcts |
ARDS |
Diffuse
infiltrate |
Diffuse alveolar damage. Microthrombosis |
|
17 |
|
|
|
VL |
|
ARDS |
|
|
|
18 |
|
|
MI, VL |
Cardiomegaly |
|
ARDS |
Basal infiltrate |
Microthrombosis |
|
19 |
|
Femoral
|
Failure MI |
AD oclussion |
AD thrombi VL |
|
|
Edema |
|
20 |
|
|
|
|
Microthrombosis |
ARDS |
|
Hyaline membrane. Intraalveolar hemorrhage |
|
21 ( 1st) |
|
|
|
|
|
|
|
|
|
(2nd) |
|
|
|
|
|
|
|
|
|
22 |
IVC
|
|
|
|
L-S Microthrombosis |
|
|
PE |
|
23 |
|
|
Failure MI |
|
microthrombosis |
|
|
PE |
|
24 |
|
|
Failure |
L-S |
L-S Microthrombosis |
ARDS |
|
Bronchopneumonia Diffuse alveolar damage Hyaline membrane |
|
25 |
|
|
|
|
|
|
|
|
|
26 |
|
|
|
|
|
ARDS
|
Alveolar hemorrhage |
|
|
27 |
|
|
Infarcts |
|
|
|
|
|
|
28 |
|
Iliac, aortic |
Failure |
|
|
Edema |
Infiltrates |
|
|
29 |
|
|
|
|
|
|
|
|
|
30 |
|
|
Failure |
Cardiomegaly |
Coronary thromosis |
|
PE |
|
|
31 |
|
|
failure |
|
|
Edema |
Bilateral infiltrates |
|
|
32 |
DVT |
|
|
|
|
|
|
|
|
33 |
|
|
|
|
|
ARDS |
Bilateral infiltrates |
|
|
34 |
|
|
|
Cardiomegaly |
|
|
Edema |
|
|
35 |
DVT |
|
|
|
|
|
|
|
|
36 |
|
|
|
|
L-S Microinfarcts |
ARDS |
|
Microthrombosis |
|
37 |
|
|
|
|
|
|
|
|
|
38 |
Jugular |
Subclavian Femoral |
MI |
|
|
|
PE |
|
|
39 |
|
|
|
|
|
|
|
|
|
40 |
|
|
|
|
|
|
Edema
|
|
|
41 |
|
|
|
|
|
ARDS
|
Bilateral infiltrates |
|
|
42 |
DVT |
|
|
|
|
|
PE |
|
|
43 |
|
|
|
|
|
ARDS
|
|
|
|
44 |
DVT |
Yes |
|
|
|
|
|
|
|
45 |
|
Yes |
|
|
|
ARDS |
|
|
|
46 |
DVT |
|
MI |
|
|
ARDS |
|
|
|
47 |
|
|
|
VL |
L-S Microthrombosis |
|
|
Edema |
|
48 |
|
|
|
|
|
ARDS |
|
Microthrombosis Alveolar hemorhhege |
|
49 |
|
|
Failure |
Dilated cardiomyopathy |
|
ARDS |
Bilateral
infiltrates |
|
|
50 |
|
|
|
|
|
PE |
|
microthrombosis |
|
51 |
Superficial femoral Popliteal |
|
|
VL |
|
|
PE |
|
|
52 |
|
|
|
|
|
|
|
|
|
53 |
|
|
MI |
|
|
ARDS |
Bilateral infiltrates |
Edema Bronchopneumonia |
|
54 |
|
|
|
L-S |
L-S Microthrombosis |
Failure |
|
Microthrombosis |
|
55 |
|
|
|
|
|
|
|
|
|
56 |
DVT |
Humeral (4) Radial |
Chest pain |
Angiogram normal |
|
|
|
|
|
57 |
|
|
MI |
|
|
Failure |
PE
|
|
|
58 |
|
|
|
|
|
|
|
|
|
59 |
|
|
failure |
cardiomyopathy |
|
ARDS |
|
|
|
60 |
|
|
|
|
|
|
|
|
|
61 |
|
|
|
LV |
|
|
|
|
|
62 |
|
|
|
|
|
ARDS |
Bilateral infiltrates |
|
|
63 |
|
Leg |
|
|
|
ARDS |
|
|
|
64 |
|
Leg |
Failure |
cardiomegaly |
|
|
PE |
|
|
65 |
IVC |
|
|
|
|
|
|
|
|
66 |
Jugular, subclavian |
Leg |
MI |
|
|
|
|
|
|
67 |
|
Subclavian |
|
|
|
|
Multiple PE |
|
|
68 |
|
|
|
|
L-S Microthrombosis |
|
|
|
|
69 |
|
|
|
|
L-S Microthrombosis |
ARDS |
Bilateral infiltrates |
Microthrombosis |
|
70(1st) |
|
|
|
|
|
|
|
|
|
(2nd) |
DVT |
|
Failure |
Cardiomegaly MI |
|
Failure |
Basal infiltrate |
|
|
(3rd) |
|
|
Failure |
Cardiomegaly |
|
Failure |
Edema PE |
|
|
71 |
|
|
|
L-S |
|
|
PE |
|
|
72 |
|
|
|
LV |
|
ARDS |
Bilateral infiltrate |
Alveolar damage Hyaline membrane |
|
73 |
|
Radial Superficial palmar arch |
|
|
|
|
|
|
|
74 |
DVT |
|
|
|
|
ARDS |
|
|
|
75 |
DVT |
|
|
|
|
|
PE
|
|
|
76 |
DVT |
|
Failure |
|
|
ARDS |
|
|
|
77 |
DVT |
|
Failure |
|
|
ARDS |
|
|
|
78 |
DVT |
|
Failure |
|
|
ARDS |
|
|
|
79 |
DVT |
|
|
|
|
|
PE
|
|
|
80 |
DVT |
|
Failure |
|
|
|
PE |
|
|
81 |
DVT |
|
|
|
|
|
PE |
|
|
82 |
|
|
|
|
|
ARDS |
|
|
|
83(1st) |
|
|
Failure |
cardiomegaly |
|
|
Edema
|
|
|
83(2nd) |
|
|
Failure |
|
|
|
Edema PE |
|
|
84 |
|
|
|
|
|
|
|
|
|
85 |
DVT |
|
Failure MI |
|
L-S Microinfarcts |
ARDS |
|
Bronchopneumonia microthrombosis |
|
86 |
|
|
|
|
|
|
PE
|
|
|
87 |
|
|
Failure MI |
Cardiomyopathy |
|
Failure |
Basal infiltrate |
|
|
88 |
|
|
|
L-S |
L-S |
ARDS |
|
|
|
89 |
|
Posterior tibial Dorsalis pedis |
|
|
|
|
|
|
|
90 |
|
|
|
|
|
|
|
|
|
91 |
|
|
|
|
|
|
PE |
Microthrombosis |
|
92 |
|
|
|
|
Micro thrombosis |
|
|
Microthrombosis |
|
93 |
|
|
Failure |
Cardiomyopathy L-S |
Micro thrombosis |
|
|
|
|
94 |
|
|
|
|
Micro thrombosis |
ARDS |
|
Microthrombosis |
|
95 |
|
|
Failure |
Cardiomyopathy |
Micro thrombosis |
|
|
Microthrombosis |
|
96 |
DVT |
|
Failure |
L-S |
L-S |
|
Multiple PE |
Microinfarcts
|
|
97 |
|
Dorsalis pedis
|
|
MI
|
|
|
|
|
|
98 |
|
|
|
|
|
|
|
|
|
99 |
|
|
Chest
pain |
|
|
ARDS |
|
|
|
100 |
|
|
|
|
|
ARDS |
|
|
|
101 |
|
Femoral
|
|
Pericardial
effusion |
|
|
Bilateral infiltrate |
|
|
102 |
|
|
|
|
|
|
|
|
|
103 |
|
|
Chest
pain |
Cardiomegaly LV |
|
Haemoptysis |
Multiple
PE |
|
|
104 |
IVC |
|
|
Hypokinesis |
|
ARDS |
PE |
|
|
105 |
|
|
|
|
|
Failure |
PE |
|
|
106 |
|
|
|
Cardiomegaly |
|
ARDS |
Bilateral
infiltrate |
|
|
107 |
|
|
Failure
|
Cardiomegaly |
Microinfarcts |
|
|
Microthrombosis |
|
108 |
DVT |
|
|
|
|
ARDS |
PE |
|
|
109 |
|
|
|
LV, MI |
|
Failure |
|
|
|
110 |
|
|
|
|
|
ARDS |
Bilateral infiltrate |
|
|
111 |
|
|
|
Atrium thrombosis |
|
|
PE
|
|
|
112 |
|
|
|
Atrium thrombosis |
|
|
Edema |
|
|
113 |
|
|
|
|
|
|
|
|
|
114 |
DVT |
|
|
LV |
|
|
|
|
|
115 |
|
|
|
|
|
|
|
|
|
116 |
|
|
|
|
|
|
|
|
|
117 |
|
|
|
|
|
|
|
|
|
118 |
DVT |
|
|
|
|
|
|
|
|
119 |
|
|
|
MI, LV |
|
|
|
|
|
120 |
DVT |
|
|
|
|
|
PE |
|
|
121 |
|
|
|
MI |
|
ARDS |
|
|
|
122 |
|
|
MI |
|
|
|
|
|
|
123 |
|
|
MI |
Hypokinesis |
|
|
|
|
|
124 |
|
|
|
MI, LV |
|
|
|
|
|
125 |
|
|
|
LV |
|
ARDS |
Bilateral infiltrate |
|
|
126 |
DVT |
|
|
|
|
Intraalveolar hemorrage |
|
|
|
127 |
|
Leg artery |
|
VL |
|
ARDS |
|
|
|
128 |
DVT |
|
|
|
|
Intraalveolar Hemorrhage+ |
|
|
|
129 |
DVT |
|
|
|
|
|
|
|
|
130 |
DVT |
|
|
VL |
|
|
|
|
|
131 |
|
|
Arrest
|
|
|
Arrest
|
PE
|
Microthrombosis
|
|
132 |
|
|
|
MI |
|
ARDS |
Infiltrate. Massive
PE |
|
|
133 |
|
|
MI |
MI,
L-S Angi
normal |
|
|
|
|
|
134 |
|
|
|
|
|
ARDS |
|
|
|
135 |
|
|
|
|
|
Failure
|
PE
|
|
|
136 |
|
|
Failure
|
VL Hypokinesis |
Microthrombosis
|
|
|
Microthrombosis
|
|
137 |
|
Humeral (2) |
|
|
|
|
|
|
|
138 |
|
|
Failure |
|
|
|
Edema
|
|
|
139 |
|
|
Failure |
Dilated cardiomyopathy |
|
|
Edema |
|
|
140 |
|
|
Failure |
Dilated carfiomyopathy Apical thrombi |
|
|
PE |
|
|
141 |
|
|
|
|
|
|
|
|
|
142 |
|
|
|
|
|
|
|
|
|
143 |
|
|
|
|
microthrombosis |
|
|
|
|
144 |
|
|
|
|
|
|
|
|
|
145 |
DVT |
|
Failure |
|
|
|
Alveolar hemorrhage |
|
|
146 |
|
|
|
|
|
|
PE |
|
|
147 |
|
|
MI |
LV, hypokinesis Oval foramen |
|
|
|
|
|
148 |
|
|
Failure |
Dilated cardiomyopathy VL |
|
Edema |
|
|
|
149 |
|
|
|
|
|
ARDS |
|
|
|
150 |
|
|
MI |
MI VL |
|
|
|
|
|
151 |
|
|
|
VL |
|
|
Alveolar hemorrhage |
|
|
152 |
|
|
Failure |
|
|
Edema |
Pulmonary hypertension |
|
|
153 |
|
|
|
|
|
|
PE |
|
|
154 |
|
|
|
VL |
|
Edema |
|
|
|
155 |
|
|
MI |
MI |
|
|
|
|
|
156 |
Subclavia, axillary, iliac,
femoral |
|
|
VL |
|
|
Bilateral PE |
|
|
157 |
Subclavian, brachiocephalic,
jugular |
|
|
VL |
|
Failure |
Bilateral PE |
|
|
158 |
Femoral |
|
MI |
MI |
|
ARDS |
|
|
|
159 |
|
|
|
Atrium thrombi |
|
Arrest |
|
Infarcts |
|
160 |
Jugular A-V fístula |
Aortic |
|
|
|
|
|
|
|
161 |
|
|
|
|
|
|
|
|
|
162 |
|
|
|
|
|
|
|
|
|
163 |
|
|
Shock |
L-S |
|
Failure |
|
|
|
164 |
|
|
|
Perivardial
effussion |
|
Failure |
|
Hemorrhage Microthrombosis |
|
165 |
|
|
|
|
|
Failure |
PE
|
|
|
166 |
Femoral, popliteal, tibial. |
|
MI |
AD trombosis. Stent thrombosis |
|
|
|
|
|
167 |
|
|
|
|
|
|
|
|
|
168 |
|
|
|
|
|
|
|
|
|
169 |
|
|
|
|
|
Failure |
Alveolar hemorrhage |
|
|
170 |
|
|
Arrest |
|
|
Arrest |
|
|
|
171 |
|
|
|
|
|
|
Alveolar hemorrhage |
|
|
172 |
|
|
|
VL |
|
|
Alveolar hemorrhage |
|
|
173 |
||||||||